Extra-abdominal Desmoid Fibromatosis
Supplemental Studies
Immunohistology
Beta-catenin | positive |
Actin | positive |
Desmin | usually negative, occasionally focal |
CD34 | negative |
S100 | negative |
Keratin | negative |
Estrogen receptor | 0-10% |
Progesterone receptor | 0-25% |
Cathepsin-D | positive |
Genetics
Trisomies 8 and 20, common in extra-abdominal desmoids are rare in abdominal desmoids