Immunophenotypic features of acute myeloid leukemia with inv(3)(q21q26.2)/t(3;3)(q21;q26.2)

Leuk Res. 2010 May;34(5):594-7. doi: 10.1016/j.leukres.2009.08.029. Epub 2009 Sep 24.

Abstract

Immunophenotypic identification of myeloid specific antigens is an important diagnostic tool in the management of patients with acute myeloid leukemia (AML). These antigens allow determination of cell of origin and degree of differentiation of leukemia blasts. AML with inv(3)(q21q26.2)/t(3;3)(q21;q26.2) is a relatively rare subtype of AML. The immunophenotypic characteristics of inv(3) AML patients are somewhat limited. We identified 14 new cases of hematological disorders with increased myeloid blasts carrying inv(3)(q21q26.2)/t(3;3)(q21;q26.2). Also, we identified another 13 cases previously published in the literature, where the immunophenotype of inv(3)(q21q26.2) was documented. As a group, patients with AML with inv(3)(q21q26.2) had high levels of early myeloid (CD13, CD33, CD117 and MPO) and uncommitted markers (CD34, HLA-DR and CD56) and a high rate of monosomy 7 in addition to the inv(3)(q21q26.2). Differential karyotype and expression of certain antigens were noted in patients with de novo AML with inv(3)(q21q26.2) vs. those with inv(3)(q21q26.2)-containing blasts.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Antigens, CD / biosynthesis
  • Cell Separation
  • Chromosome Inversion
  • Female
  • Flow Cytometry
  • HLA-DR Antigens / genetics
  • Humans
  • Immunophenotyping
  • Kaplan-Meier Estimate
  • Karyotyping
  • Leukemia, Myeloid, Acute / classification
  • Leukemia, Myeloid, Acute / genetics*
  • Leukemia, Myeloid, Acute / immunology*
  • Male
  • Middle Aged
  • Oncogene Proteins, Fusion / genetics
  • Prognosis
  • Young Adult

Substances

  • Antigens, CD
  • HLA-DR Antigens
  • Oncogene Proteins, Fusion
  • RPN1-EVI1 fusion protein, human